A rare case of obstructed hemivagina and ipsilateral renal agenesis syndrome presented with haematocolpos and haematometra

Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a characterised by obstructed hemivagina, agenesis uterine didelphys. It rare congenital results from defective fusion of the Müllerian ducts during development female reproductive system. also known as Herlyn-Werner-Wunderlich syndrome. Aim study was to project case developmental Mullerian OHVIRA anomaly. The most common presentation this mass secondary hematocolpos, pain, dysmenorrhea. Incidence rate 0.1-3%. Other symptoms are swelling abdomen, nausea vomiting due pelvic fertility may be affected. Diagnosed magnetic resonance imaging (MRI) ultrasound. This managed diagnostic laparoscopy with resection vertical vaginal septum. treatment option vaginoscopic incision oblique High level clinical suspicion early surgical intervention will prevent further complications.